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consider a new option for your LC-FAOD

The first and only FDA-approved treatment for children and adults with long-chain fatty acid oxidation disorders.

Select a type to learn more.

consider a new option for your LC-FAOD.

The first and only FDA-approved treatment for children and adults with long-chain fatty acid oxidation disorders.

Select a type to learn more.

CPT I(carnitine palmitoyltransferase I) deficiency

consider a new option for your LC-FAOD

STARTING DOJOLVI

UltraCare® Patient Services is here to help you:

  • Gain access to DOJOLVI
  • Understand your insurance coverage
  • Determine your eligibility for financial and patient assistance programs
  • Utilize patient support program resources

Visit UltraCare

A completed Start Form is required for enrollment in UltraCare Patient Services. Talk to your healthcare team.

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TAKING DOJOLVI

Download a step-by-step guide for how to store, administer, and keep track of DOJOLVI doses.

Download the Guide

LC-FAOD defined.

WHAT ARE LC-FAOD?

Long-chain fatty acid oxidation disorders (LC-FAOD) are rare inherited disorders that prevent the body from breaking down long-chain fatty acids into energy during metabolism.

Each type of LC-FAOD is named for the specific enzyme that is affected.

People living with LC-FAOD have difficulty producing enough energy because of their body’s inability to use long-chain fatty acids as an energy source during times of:

  • Fasting
  • Illness
  • Prolonged exercise

Select a type to learn more.

CPT I(carnitine palmitoyltransferase I) deficiency

Meet DOJOLVI (triheptanoin).

WHAT IS DOJOLVI?

DOJOLVI is a prescription medicine used to treat long-chain fatty acid oxidation disorders (LC-FAOD) in children and adults.

How does DOJOLVI work?

  • DOJOLVI provides an alternate source of energy. It is a synthetic medium odd-chain 7-carbon triglyceride (C7).
  • DOJOLVI bypasses the enzyme deficiencies that cause LC-FAOD to provide a source of calories and fatty acids that can be converted to energy.

Talk to your healthcare team to learn more about DOJOLVI.

WHAT IS DOJOLVI?

Taking DOJOLVI (triheptanoin).

Always take DOJOLVI exactly as your LC-FAOD healthcare team advises

doctor icon

Before taking DOJOLVI, tell your healthcare provider about all of your medical conditions, including if you:

  • are pregnant or plan to become pregnant. It is not known if DOJOLVI will harm your unborn baby
  • are breastfeeding or plan to breastfeed. It is not known if DOJOLVI passes into breast milk
  • are taking a pancreatic lipase inhibitor, such as orlistat, as it may affect how well DOJOLVI works

Tell your healthcare provider about all the medicines you take, including prescription and over-the-counter medicines, vitamins, and herbal supplements.

mct icon

If you are taking another medium-chain triglyceride (MCT) formulation, stop taking the MCT before starting DOJOLVI

syringe icon

Use an oral syringe or a measuring cup to measure the prescribed dose of DOJOLVI

do not icon

Do not mix or give DOJOLVI using containers, dosing syringes, or measuring cups made of polystyrene (a type of plastic that can be solid or foam) or polyvinyl chloride (PVC), a solid plastic material

mix icon

Mix or give DOJOLVI using containers, dosing components, or utensils made of materials such as stainless steel, glass, or high-density polyethylene (HDPE), polypropylene, low-density polyethylene (LDPE), polyurethane, and silicone (types of plastic materials)

daily dose icon

DOJOLVI should be taken at least 4 times a day with meals or snacks, and always mixed well with soft food or drink

drink icon

DOJOLVI can be mixed with the following soft food or drink:

  • Plain or artificially sweetened fat-free yogurt
  • Fat-free milk, formula, or cottage cheese
  • Whole-grain hot cereal
  • Fat-free, low-carbohydrate pudding, smoothies, applesauce, or baby food

The mixture may be stored for up to 24 hours in the refrigerator

Feeding tubes may not work as well or stop working over time when taking DOJOLVI. Do not use DOJOLVI in feeding tubes made of polyvinyl chloride (PVC). Monitor the feeding tube to make sure it is working properly.

If you miss a dose, take the next dose as soon as possible. Take the following doses 3 to 4 hours apart. If it is not possible to take all the doses for the day, skip the missed dose.

Speak to your healthcare team and see the Instructions for Use included in the Patient Information Leaflet for more information.

storing dojolvi

temperature icon

Store DOJOLVI upright at room temperature between 68° and 77°F (20° and 25°C)

do not freeze icon

Do not freeze DOJOLVI

expire icon

When the bottle of DOJOLVI has been opened, use within 9 months or by the expiration date on the bottle, whichever comes first

caution icon

Do not store product in containers made of polystyrene or polyvinyl chloride (PVC)

DOJOLVI™ (triheptanoin) product image

dosing guide

Learn how to store, administer, and keep track of DOJOLVI doses.

DOJOLVI™ (triheptanoin) Dosing Guide

Download the Guide

TRACKING DAILY DOSES

It’s important to stick with your treatment plan.
Frequent monitoring, especially as you begin taking DOJOLVI, can:

  • Help you adapt to and maintain your treatment plan
  • Help your healthcare team decide if any dosing modifications are needed

Track your doses in 3 easy steps.

1

 

2

 

3

1. DIVIDE

Divide the prescribed daily amount of DOJOLVI by at least 4 to determine each dose amount.

Ex: 56 mL/4 = 14 mL per dose

2. RECORD

Recording the exact time you take your doses will help you track medication for the day.

3. NOTE

Use the notes section to communicate important information to your healthcare team.

EXAMPLE: Not actual patient data; for illustrative purposes only.

DOJOLVI™ (triheptanoin) Daily Dosing Tracker

Download the Daily Dosing Tracker >

WORKING WITH YOUR HEALTHCARE TEAM

All patients treated with DOJOLVI should be under the care of clinical specialists knowledgeable in appropriate disease-related dietary management based upon current nutritional recommendations.

These specialists, which may include metabolic geneticists, dietitians, and nurse practitioners, will work together as your healthcare team and:

  • May start you on a low dose of DOJOLVI and slowly increase your dose to help avoid side effects
  • Ensure you are receiving frequent monitoring and nutritional counseling appropriate to your specific needs when taking DOJOLVI

Stay Informed

Connect with us to get the latest information on DOJOLVI from Ultragenyx.

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By submitting this form, you agree to allow Ultragenyx and its agents to collect the information provided and to be contacted directly by an Ultragenyx representative. Your information will not be used for any other purpose than for a representative to respond to your information request or for us to send you other DOJOLVI updates if you have registered to receive them.

Ultragenyx will not sell, rent, or otherwise distribute your name and any personally identifiable information outside of Ultragenyx and its agents. Ultragenyx will only use your information in accordance with its Privacy Policy.

What is DOJOLVI?

DOJOLVI is a prescription medicine used to treat long-chain fatty acid oxidation disorders (LC-FAOD) in children and adults.

IMPORTANT SAFETY INFORMATION

What are the possible side effects of DOJOLVI?

  • Feeding tube problems. Feeding tubes may not work as well or stop working over time when taking DOJOLVI. Do not use DOJOLVI in feeding tubes made of polyvinyl chloride (PVC), a solid plastic material. Monitor the feeding tube to make sure it is working properly.
  • Intestinal absorption problems in patients with pancreatic insufficiency. If you have pancreatic insufficiency, consult with your healthcare provider as it may affect how well DOJOLVI works.
  • The most common side effects of DOJOLVI are:
    • stomach (abdominal) pain
    • diarrhea
    • vomiting
    • nausea

These are not all the possible side effects of DOJOLVI. Call your healthcare provider for medical advice about side effects. You may report side effects to Ultragenyx Pharmaceutical Inc. at 1-888-756-8657 or FDA at 1-800-FDA-1088.

Before taking DOJOLVI, tell your healthcare provider about all of your medical conditions, including if you:

  • are pregnant or plan to become pregnant. It is not known if DOJOLVI will harm your unborn baby. Pregnancy Safety Study: There is a pregnancy safety study for women who take DOJOLVI during pregnancy. The purpose of this study is to collect information about your health and your baby's health. You can talk to your healthcare provider or contact 1-888-756-8657 to enroll in this study or get more information.
  • are breastfeeding or plan to breastfeed. It is not known if DOJOLVI passes into breast milk. Talk to your healthcare provider about the best way to feed your baby if you take DOJOLVI.
  • are taking a pancreatic lipase inhibitor, such as orlistat, as it may affect how well DOJOLVI works.

Tell your healthcare provider about all the medicines you take, including prescription and over-the-counter medicines, vitamins, and herbal supplements.

How should I take DOJOLVI?

  • See the detailed "Instructions for Use" at the end of the Patient Information Leaflet for instructions about how to mix and take DOJOLVI by mouth in soft foods or drinks or how to mix and give DOJOLVI through feeding tubes.
  • Take DOJOLVI exactly as your healthcare provider tells you.
  • Your healthcare provider may start you on a low dose of DOJOLVI and slowly increase your dose to help avoid side effects. If you are taking another medium chain triglyceride (MCT) product, stop taking the MCT before starting DOJOLVI.

Please see full Prescribing Information, including the Patient Information Leaflet, for additional Important Safety Information.

What is DOJOLVI?

DOJOLVI is a prescription medicine used to treat long-chain fatty acid oxidation disorders (LC-FAOD) in children and adults.

IMPORTANT SAFETY INFORMATION

What are the possible side effects of DOJOLVI?

  • Feeding tube problems. Feeding tubes may not work as well or stop working over time when taking DOJOLVI. Do not use DOJOLVI in feeding tubes made of polyvinyl chloride (PVC), a solid plastic material. Monitor the feeding tube to make sure it is working properly.
  • Intestinal absorption problems in patients with pancreatic insufficiency. If you have pancreatic insufficiency, consult with your healthcare provider as it may affect how well DOJOLVI works.
  • The most common side effects of DOJOLVI are:
    • stomach (abdominal) pain
    • diarrhea
    • vomiting
    • nausea

These are not all the possible side effects of DOJOLVI. Call your healthcare provider for medical advice about side effects. You may report side effects to Ultragenyx Pharmaceutical Inc. at 1-888-756-8657 or FDA at 1-800-FDA-1088.

Before taking DOJOLVI, tell your healthcare provider about all of your medical conditions, including if you:

  • are pregnant or plan to become pregnant. It is not known if DOJOLVI will harm your unborn baby. Pregnancy Safety Study: There is a pregnancy safety study for women who take DOJOLVI during pregnancy. The purpose of this study is to collect information about your health and your baby's health. You can talk to your healthcare provider or contact 1-888-756-8657 to enroll in this study or get more information.
  • are breastfeeding or plan to breastfeed. It is not known if DOJOLVI passes into breast milk. Talk to your healthcare provider about the best way to feed your baby if you take DOJOLVI.
  • are taking a pancreatic lipase inhibitor, such as orlistat, as it may affect how well DOJOLVI works.

Tell your healthcare provider about all the medicines you take, including prescription and over-the-counter medicines, vitamins, and herbal supplements.

How should I take DOJOLVI?

  • See the detailed "Instructions for Use" at the end of the Patient Information Leaflet for instructions about how to mix and take DOJOLVI by mouth in soft foods or drinks or how to mix and give DOJOLVI through feeding tubes.
  • Take DOJOLVI exactly as your healthcare provider tells you.
  • Your healthcare provider may start you on a low dose of DOJOLVI and slowly increase your dose to help avoid side effects. If you are taking another medium chain triglyceride (MCT) product, stop taking the MCT before starting DOJOLVI.

Please see full Prescribing Information, including the Patient Information Leaflet, for additional Important Safety Information.